Myotonic Dystrophy type 1, individualised respiratory care rather than standart prognostication

Published:April 17, 2019DOI:https://doi.org/10.1016/j.jns.2019.04.020
      We read with interest the article “Prevalence and predictor factors of respiratory impairment in a large cohort of patients with Myotonic Dystrophy type 1 (DM1): A retrospective, cross sectional study” by Rossi et al. [
      • Rossi S.
      • Della Marca G.
      • Ricci M.
      • Perna A.
      • Nicoletti T.F.
      • Brunetti V.
      • Meleo E.
      • Calvello M.
      • Petrucci A.
      • Antonini G.
      • Bucci E.
      • Licchelli L.
      • Sancricca C.
      • Massa R.
      • Rastelli E.
      • Botta A.
      • Di Muzio A.
      • Romano S.
      • Garibaldi M.
      • Silvestri G.
      Prevalence and predictor factors of respiratory impairment in a large cohort of patients with Myotonic Dystrophy type 1 (DM1): a retrospective, cross sectional study.
      ].

      Keywords

      Abbreviations:

      DM1 (Myotonic Dystrophy type 1), FVC (forced vital capacity), HCVR (hypercapnic ventilator response), NIV (non invasive ventilation), NMD (neuromuscular disorders)
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