The frequency of neurologic manifestations in Behçet's disease (BD) ranges between
5% and 15% [
[1]
]. Central nervous system manifestations are represented by parenchymal involvement,
which includes brainstem involvement, hemispheric manifestations, spinal cord lesions,
and meningo-encephalitic presentations and non parenchymal involvement, including
dural sinus thrombosis, arterial occlusion, and/or aneurysms. The association of parenchymal
and vascular manifestations is extremely rare [
[2]
]. Among the neuro-vasculo-Behçet's disease patients, venous thrombosis is well-known
while arterial involvement has rarely been reported and seldom concerned cerebral
arteries. We describe here a stroke case revealing neuro-Behçet's disease (NBD) with
parenchymal involvement and extensive vascular lesions interesting several intracranial
and systemic arteries. To the best of our knowledge, this is the first reported case
of Behçet's disease manifesting as concomitant involvement of systemic and cerebral
arteries.Keywords
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Article info
Publication history
Published online: January 26, 2019
Accepted:
January 25,
2019
Received:
November 19,
2018
Identification
Copyright
© 2019 Elsevier B.V. All rights reserved.
