Highlights
- •Consider a leukodystrophy in patients with a ‘refractory’ cerebral vasculitis
- •CSF1R mutation analysis and a brain biopsy are often required to exclude mimics
- •ALSP may present with early onset dementia and personality changes
- •A progressive motor and gait disturbance is often seen, occasionally with seizures
Keywords
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References
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Article info
Publication history
Published online: September 22, 2018
Accepted:
September 21,
2018
Received in revised form:
September 20,
2018
Received:
July 5,
2018
Identification
Copyright
Crown Copyright © 2018 Published by Elsevier B.V. All rights reserved.