Gastrointestinal compromise in Susac Syndrome

  • Mariano Marrodan
    Correspondence
    Corresponding author at: Montañeses 2325, Buenos Aires PC C1428AQK, Argentina.
    Affiliations
    Department of Neurology, Institute for Neurological Research Raúl Carrea, Fundación para la lucha de las enfermedades neurológicas de la infancia (FLENI), Buenos Aires, Argentina
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  • J. Correale
    Affiliations
    Department of Neurology, Institute for Neurological Research Raúl Carrea, Fundación para la lucha de las enfermedades neurológicas de la infancia (FLENI), Buenos Aires, Argentina
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  • L. Alessandro
    Affiliations
    Department of Neurology, Institute for Neurological Research Raúl Carrea, Fundación para la lucha de las enfermedades neurológicas de la infancia (FLENI), Buenos Aires, Argentina
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  • N. Arakaki
    Affiliations
    Department of Pathology, Institute for Neurological Research Raúl Carrea, FLENI, Buenos Aires, Argentina
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  • R. Rennebohm
    Affiliations
    Susac Syndrome Consultation Service, Cleveland Clinic, Cleveland, OH, United States
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  • A.A. Kohler
    Affiliations
    Department of Neurology, Institute for Neurological Research Raúl Carrea, Fundación para la lucha de las enfermedades neurológicas de la infancia (FLENI), Buenos Aires, Argentina
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  • M.P. Fiol
    Affiliations
    Department of Neurology, Institute for Neurological Research Raúl Carrea, Fundación para la lucha de las enfermedades neurológicas de la infancia (FLENI), Buenos Aires, Argentina
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      Highlights

      • This is the first report of Susac Syndrome and ischemic colitis.
      • Common pathophysiological mechanisms are proposed.
      • The possibility of escalation of immunosuppressive treatment might be analyzed.
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