Neuronal intranuclear hyaline inclusion disease (NIHID) or neuronal intranuclear inclusion
disease (NIID) is a rare neurodegenerative disorder characterized by intranuclear
inclusions (IIs) in neuronal and glial cells [
1
,
2
]. Here we report distinctive clinico-pathological findings of a sporadic case of NIHID,
who had the transient improvement and episodic exacerbations of the clinical symptoms
during the course and mitochondrial abnormality.Keywords
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Article info
Publication history
Published online: October 27, 2016
Accepted:
October 25,
2016
Received in revised form:
September 25,
2016
Received:
May 25,
2016
Identification
Copyright
© 2016 Elsevier B.V. All rights reserved.
