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Short communication| Volume 324, ISSUE 1-2, P187-189, January 15, 2013

Susac's syndrome: A case of simultaneous development of all three components of the triad

Published:November 12, 2012DOI:https://doi.org/10.1016/j.jns.2012.10.019

      Abstract

      Susac's syndrome is characterized by the clinical triad of encephalopathy, branch retinal artery occlusions and sensorineural hearing loss. We here report a case of 46 year old woman with a sudden diminution in visual acuity at the left eye, headache and decreased hearing at the right ear with mild confusion considered as Susac's syndrome with complete triad. Although it's a relatively rare entity, it should be kept in mind in differential diagnosis of the neurological disorders, especially in women in 20- to 40-year of age presenting with acute hearing loss.

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