Abstract
Susac's syndrome is characterized by the clinical triad of encephalopathy, branch
retinal artery occlusions and sensorineural hearing loss. We here report a case of
46 year old woman with a sudden diminution in visual acuity at the left eye, headache
and decreased hearing at the right ear with mild confusion considered as Susac's syndrome
with complete triad. Although it's a relatively rare entity, it should be kept in
mind in differential diagnosis of the neurological disorders, especially in women
in 20- to 40-year of age presenting with acute hearing loss.
Keywords
To read this article in full you will need to make a payment
Purchase one-time access:
Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online accessOne-time access price info
- For academic or personal research use, select 'Academic and Personal'
- For corporate R&D use, select 'Corporate R&D Professionals'
Subscribe:
Subscribe to Journal of the Neurological SciencesAlready a print subscriber? Claim online access
Already an online subscriber? Sign in
Register: Create an account
Institutional Access: Sign in to ScienceDirect
References
- Microangiopathy of the brain and retina.Neurology. 1979; 29: 313-316
- Susac syndrome.Intern Med. 2010; 49: 1685-1686
- Retinal vasculitis in Susac syndrome: case report.Arq Bras Oftalmol. May-Jun 2009; 72: 397-399
- Susac syndrome as an example of a rare vasculopathy.Pol Arch Med Wewn. Jan-Feb 2009; 119: 80-82
- Microangiopathy of the brain and retina with hearing loss in a 50 year old woman: extending the spectrum of Susac's syndrome.J Neurol Neurosurg Psychiatry. 1999; 66: 641-643
- Susac's syndrome: the triad of microangiopathy of the brain and retina with hearing loss in young women.Neurology. 1994; 44: 591-593
- Patterns of retinal damage facilitate differential diagnosis between Susac syndrome and MS.PLoS One. 2012; 7: e38741
- Microangiopathy of the brain and retina (Susac's syndrome): two patients with atypical features.Neurology. 1995; 45: 1225-1226
- Microangiopathy of the brain, retina and ear: improvement without immunosuppressive therapy.Stroke. 1991; 22: 933-937
- A microangiopathic syndrome of encephalopathy, hearing loss, and retinal arteriolar occlusions.Neurology. 1985; 35: 1113-1121
- Small infarctions of cochlear, retinal and encephalic tissue in young women.Stroke. 1992; 23: 903-907
- Susac's syndrome or retinocochlcocerebral vasculopathy: a misdiagnosed and overlooked disorder.Eur J Intern Med. 2000; 11: 108-111
- Microangiopathy with retinopathy, encephalopathy and deafness (RED-M) and systemic features.Semin Arthritis Rheum. 1991; 21: 123-128
- Retinal arterial wall plaques in Susac syndrome.Am J Ophthalmol. 2003; 132: 483-486
- Susac syndrome.Am J Ophthalmol. 2000; 129: 682-684
- Microangiopathy of the inner ear, retina and brain (Susac syndrome).Arch Otolaryngol Head Neck Surg. 2000; 126: 82-84
- Susac syndrome: a vasospastic disorder?.Eur J Ophthalmol. 2001; 11: 175-179
- Encephalopathy, deafness and blindness in young women: a distinct retinocochleocerebral arteriopathy?.J Neurol Neurosurg Psychiatry. 1989; 35: 114-117
- Recurrence of Susac syndrome (retinocochleocerebral vasculopathy).Mayo Clin Proc. 2001; 76: 958-960
Article info
Publication history
Published online: November 12, 2012
Accepted:
October 22,
2012
Received in revised form:
September 18,
2012
Received:
January 25,
2012
Identification
Copyright
© 2012 Elsevier B.V. Published by Elsevier Inc. All rights reserved.