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Abstract
The authors report a case of non-progressive, late-onset, recessive, sex-linked myopathy.
Electron microscopy reveals a striking proliferation of the T system. This proliferation
might be interpreted as indicating an abortive attempt of muscle to regenerate, which
could explain the clinical course.
Some basic ultrastructural aspects concerning the T system are reported. The significantion
of the findings of numerous “zebra bodies” is discussed.
Résumé
Les auteurs relatent une observation de dystrophie musculaire peu progressive à début
tardif, à transmission récessive et liée au sexe.
Une extrême prolifération du système T est observée en microscopie électronique. Elle
est interprétée comme une tentative avortée de régénération du muscle, susceptible
de rendre compte de l'évolution clinique.
Quelques points d'ultrastructure fondamentale du tube T sont abordés. La signification
de nombreux “corps zébrés” est discutée.
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Article info
Publication history
Received:
August 6,
1975
Footnotes
☆Ce travail a bénéficié de l'aide de l'Association Lyonnaise pour la Recherche Neuropathologique.
Identification
Copyright
© 1976 Published by Elsevier Inc.
